Table 2.

Recommended surveillance protocol for HLRCC

Screening modalityAge to begin surveillanceFrequency
MRI with renal protocolAt age 8Annual
Skin checks by pediatrician, dermatology as neededAt time of diagnosisAnnual
Gynecologic exam, ultrasound as neededAge 20 or at the time of first gynecologic exam, earlier if symptomsAnnual